Desmoplastic fibroma of bone is an extremely rare and locally agressive fibroblastic tumor. It was first named and reported by Jaffe in 1958. Authors experienced a case of the tumor arising in proximal fibula. To the best of our knowledge, the
present
case is the 5th one reported in Korea and the first one occured in fibula.
A 27 years old woman first presented in November 1989 with a 3-years complaint of pain, insidious in onset, in the lateral aspect of right calf. There was no previous history of trauma. Roentgen-ographic studies showed an ovoid radiolucent, well
defined
expansile lesion in the proximal fibula, with a trabeculation. A provisional diagnosis of aneurysmal bone cyst was made and en bloc excision was done.
Gross examination of the tumor after excision revealed the grayish white colored firm, rubbery hard mass with no evidence of ossification, measuring 8×2.5×2 cm. the microscopic study showed elongated, spindle shaped cells of fibroblastic
appearance
surrounded by abundant collagen fibers running in all directions. The nuclei were monotonous and no mitotic figure was found. There was no evidence of bone or cartilage formation, and no multinucleated giant cells.
Two years postoperatively, the patient remains asymptomatic and there is no evidence of recurrence.
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